Skip to main content
Log in

Case Report: Fulminant Wilsonian Hepatitis Unmasked by Disease Progression Report of a Case and Review of the Literature

  • Published:
Digestive Diseases and Sciences Aims and scope Submit manuscript

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

REFERENCES

  1. Wilson SAK: Progressive lenticular degeneration: A familial nervous disease associated with cirrhosis of the liver. Brain 34:295–509, 1912

    Google Scholar 

  2. Berman DH, Leventhal RJ, Gavaler JS, Cadoff EM, Van Thiel DH: Clinical differentiation of fulminant Wilsonian hepatitis from other causes of hepatic failure. Gastroenterology 100:1129–1134, 1991

    Google Scholar 

  3. Walshe JM: Wilson's disease presenting with features of hepatic dysfunction. Q J Med 70:253–263, 1989

    Google Scholar 

  4. Rector WG, Uchida T, Kanel GC, Redeker AG, Reynolds TB: Fulminant hepatic and renal failure complicating Wilson's disease. Liver 4:341–347, 1984

    Google Scholar 

  5. McCullough AJ, Wiesner RH, Fleming CR, Dickson ER: Antemortem diagnosis and shortterm survival of a patient with Wilson's disease presenting as fulminant hepatic failure. Dig Dis Sci 29:862–864, 1984

    Google Scholar 

  6. Schilsky ML, Scheinberg IH, Sternlieb I: Prognosis of Wilsonian chronic active hepatitis. Gastroenterology 100:762–767, 1991

    Google Scholar 

  7. Johnson PJ, Williams R: Excellent prognosis in Wilsonian chronic active hepatitis: New data or an article of faith? Hepatology 14:1293–1295, 1991

    Google Scholar 

  8. Zilker TR, Felgenhauer N, Hibler A, von Charmann CM: Indications for liver transplantation in Wilson's disease with a fulminant course. Dtch Med Wochenschr 114:871–875, 1989

    Google Scholar 

  9. Davies SE, Williams R, Portmann B: Hepatic morphology and histochemistry of Wilson's disease presenting as fulminant hepatic failure: A study of 11 cases. Histopathology 15:385–394, 1989

    Google Scholar 

  10. Gur H, Aderka D, Finkelstein A, Yoram L: Fulminant Wilsonian hepatitis: Difficulties in diagnosis and treatment. Am J Gastroenterol 83:679–681, 1988

    Google Scholar 

  11. Fleming CR, Dickson ER, Wahner HW, Hollenhorst RW: Pigmented corneal rings in non-Wilsonian liver disease. Am Intern Med 86:285–288, 1977

    Google Scholar 

  12. Kaplinsky C, Sternlieb I, Javitt N, Rotem Y: Familial cholestatic cirrhosis associated with Kayser-Fleischer rings. Pediatrics 65:782–788, 1980

    Google Scholar 

  13. Sallie R, Katsiyiannakis L, Baldwin D, Davies S, O'Grady J, Mowat A, Mieli-Vergani G, Williams R: Failure of simple biochemical indexes to reliably differentiate fulminant Wilson's disease from other causes of fulminant liver failure. Hepatology 16:1206–1211, 1992

    Google Scholar 

  14. Schilsky ML, Scheinberg IH, Sternlieb I: Prognosis of Wilsonian chronic active hepatitis. Gastroenterology 100:762–767, 1991

    Google Scholar 

  15. Walshe JM, Briggs J: Ceruloplasmin in liver disease: a diagnostic pitfall. Lancet 2:263–265, 1962

    Google Scholar 

  16. McCullough AJ, Fleming R, Thistle JL, Baldus WP, Ludwig J, McCall JT, Dickson R: Diagnosis of Wilson's disease presenting as fulminant hepatic failure. Gastroenterology 84:161–167, 1983

    Google Scholar 

  17. Nazer H, Ede RJ, Mowat AP, Williams R: Wilson's disease: Clinical presentation and use of prognostic index. Gut 27:1377–1381, 1986

    Google Scholar 

  18. Deiss A, Lee GR, Carwright GE: Hemolytic anemia in Wilson's disease. Ann Intern Med 73:413–418, 1979

    Google Scholar 

  19. Chan TK, Todd D: Haemolysis complicating viral hepatitis in patients with glucose-6-phosphate dehydrogenase deficiency. Br Med J 1:131–133, 1975

    Google Scholar 

  20. O'Grady JG, Fagan EA, Williams R: Fulminant viral hepatitis. Clin Trop Med Communic Dis 1:361–376, 1986

    Google Scholar 

  21. Lashner BA, Jones RB, Tang HS, Evans AA, Ozeran SE, Baker AL: Chronic hepatitis: Disease factors at diagnosis predictive of mortality. Am J Med 85:609–614, 1988

    Google Scholar 

  22. Scheinberg IH, Sternlieb I, Schilsky ML, Stockert RJ: Penicillamine may detoxify copper in Wilson's disease. Lancet 2:95, 1987

    Google Scholar 

  23. Durand F, Bernuan J, Samuel D, Saliba F, Shouval D, Benhamou JP: Severe acute Wilson's disease: an indication for emergency administration of high dose D-penicillamine. J Hepatol 11(suppl 2):S20, 1990

    Google Scholar 

  24. Walshe JM: Diagnosis and treatment of presymptomatic Wilson's disease. Lancet 11:435–437, 1988

    Google Scholar 

  25. Ludwig J, Mayer TP, Rakela J: The liver biopsy diagnosis of Wilson's disease: Methods in pathology. Am J Clin Pathol 102:443–446, 1994

    Google Scholar 

  26. Zilker TR, Felgenhauer N, Hibler A, von Clarmann CM: Indications for liver transplantation in Wilson's disease with a fulminant course. Dtsch Med Wochenschr 114:871–875, 1989

    Google Scholar 

Download references

Authors

Rights and permissions

Reprints and permissions

About this article

Cite this article

Ferlan-Marolt, V., Stepec, S. Case Report: Fulminant Wilsonian Hepatitis Unmasked by Disease Progression Report of a Case and Review of the Literature. Dig Dis Sci 44, 1054–1058 (1999). https://doi.org/10.1023/A:1026637403894

Download citation

  • Issue Date:

  • DOI: https://doi.org/10.1023/A:1026637403894

Navigation